| |
| | Answer C005 |
 | | Patients with the complete syndrome have pachydermia, periostitis and cutis verticis gyrata; those with the the incomplete form exhibit sparing of the scalp; and the forme fruste is manifested by pachydermia and minimal or absent periostitis. |
 | | Cutis verticis gyrata (undulating grooved and thickened scalp) may become apparent during adolescence. |
 | | Rosenfeld-Kloepfer syndrome, a variant of PDP, is characterized by enlargement of the mandible and/or the maxilla; large hands, feet, nose, lips, and tongue; prominence of the upper part of the forehead; cutis verticis gyrata; and corneal leukoma. |
| www.brts.pwp.blueyonder.co.uk /answer_c005.htm (1979 words) |
|