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Rev Electron Biomed / Electron J Biomed 2003;1(2):95-100. Ibañez-Valdés et al. RENOVASCULAR HYPERTENSION ... IN ... |
 | | Klippel-Trenaunay syndrome or Klippel-Trenaunay-Weber syndrome (KTWS) is generally accepted, when there are enlargement of the soft tissue, bony hypertrophy, port-wine stain, venous malformations and lymphatic abnormalities; in our patient we could not investigate arterio-venous fistulae by phlebography and arteriography because patient died after the surgical revascularization due to anesthetic and pulmonary complications. |
 | | Alagille syndrome with associated renovascular hypertension should also be distinguished, the association of at least three of the following five abnormalities characterizes it: chronic cholestasis, peripheral pulmonary stenosis, vertebral arch defects, embryotoxon, and typical facies. |
 | | Patients with Klippel-Feil Syndrome may be at increased of risk of significant genitourinary tract anomalies as ectopic kidney and renal agenesis, and have increase chance of developing nephrolitiasis. |
| www.biomed.uninet.edu /2003/n2/ibanezv.html (2952 words) |
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