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eMedicine - Von Hippel-Lindau Syndrome : Article by Ali Nawaz Khan, MBBS, LRCP, FRCS, FRCP, FRCR |
 | | Synonyms and related keywords: angiomatosis retinae, cerebelloretinal angiomatosis, hemangioblastomatosis cerebelloretinae, Hippel's syndrome, Hippel-Czermak syndrome, Lindau-von Hippel syndrome, retinocerebellar angiomatosis, inherited neurocutaneous dysplasia complex, angioreticuloma, spinal hemangioblastoma, endolymphatic sac tumor, cerebellopontine angle ceruminoma, external choroid plexus, extradural choroid plexus papilloma, Lindau tumor |
 | | CNS hemangioblastoma (Lindau tumor) is the most commonly recognized manifestation of VHL and occurs in 40% of patients. |
 | | Symptoms often begin in the second to third decades of life. |
| www.emedicine.com /radio/topic742.htm (4081 words) |
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