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Jornal Brasileiro de Pneumologia Mounier-Kuhn syndrome, or tracheobronchomegaly, is a rare clinical entity characterized by abnormal dilation of the trachea and main bronchi. At that point, the patient was submitted to a computed tomography scan of the chest, which revealed that the areas of consolidation, although smaller in size, persisted in both lower lobes, and confirmed the abnormal widening of the trachea and main bronchi (Figures 1, 2 and 3). Although the etiology of Mounier-Kuhn syndrome remains unknown, it is believed that it is related to a lack of smooth muscle and elastic connective tissue in the trachea and main bronchi, leading to herniation and even to the formation of diverticula between the cartilaginous rings. www.jornaldepneumologia.com.br /english/artigo_print.asp?id=275   (1364 words)

The Indian Journal of Chest Diseases and Allied Sciences   (Site not responding. Last check: 2007-10-26) The Mounier-Kuhn syndrome is a congenital abnormality characterized by atrophy or absence of elastic fibres and thinning of smooth muscle layer in trachea and main bronchi. The Mounier-Kuhn syndrome is a congenital abnormality of the trachea and main bronchi characterized by atrophy or absence of elastic fibers and thinning of muscle, which allows the trachea and the main bronchi to become flaccid and markedly dilated on inspiration with narrowing or collapse on expiration or cough. In conclusion, the diagnosis of Mounier-Kuhn syndrome should be considered in patients with recurrent pneumonia, mucus plugging and as a cause of chronic respiratory failure in young adults. www.indegene.com /ijcd/JulSept2002/article9.html   (1273 words)

KCS - Kenny-Caffey syndrome Kenny-Caffey Syndrome is a rare syndrome characterized by growth retardation, uniformly small slender long bones with medullary stenosis, thickened cortex of the long bones, hypocalcemia possibly with tetany at an early age, hyperphosphatemia, ocular abnormalities, and normal intelligence. Kenny-Caffey syndrome (KCS) is an osteosclerotic bone dysplasia with associated hypocalcemia and ocular abnormalities. The Mounier-Kuhn syndrome in a patient with the Kenny-Caffey syndrome. www.ihop-net.org /UniPub/iHOP/gi/89645.html   (198 words)

THE MERCK MANUAL, Sec. 6, Ch. 70, Bronchiectasis In these syndromes, structural or functional abnormalities in ciliary organelles result in defective mucociliary clearance that leads to suppurative bronchial infections and bronchiectasis as well as chronic rhinitis, serous otitis media, male sterility, corneal abnormalities, sinus headaches, and a poor sense of smell. Absent are the ciliary abnormalities seen in the PCD syndromes, the genetic and electrolyte abnormalities characteristic of cystic fibrosis, and the genetic mutations found in congenital absence of the vas deferens, which accounts for about 6% of obstructive azoospermia. The yellow nail syndrome, believed to be due to a congenital hypoplasia of the lymphatic system, is recognized by thickened, curved, yellowish to greenish nails (see Plate 70-1) and primary lymphedema. www.merck.com /mrkshared/mmanual/section6/chapter70/70a.jsp   (3323 words)

Jornal Brasileiro de Pneumologia A 40-year-old fl male patient was referred to the pulmonology clinic due to fatigue upon exertion and persistent dry cough three weeks after having been discharged from the hospital, where he had been admitted for treatment of pneumonia. Congenital tracheobronchomegaly, or Mounier-Kuhn syndrome, is a rare clinical entity, described for the first time in 1932,(1) and characterized by marked tracheobronchial dilation and lower respiratory tract infections. We believe that, in the case in question, the syndrome was responsible for the inappropriate response to the appropriate antibiotic therapy, which led us to suspect of a structural abnormality of the airways. www.jornaldepneumologia.com.br /english/artigo_detalhes.asp?id=275   (1393 words)

PCCU Lesson 12, Volume 17 Williams-Campbell syndrome refers to severe deficiency of airway cartilages, particularly in the segmental and distal bronchi. Tracheobronchomegaly is a rare condition characterized by dilatation of the tracheobronchial tree and recurrent bouts of bronchitis and lung infections. The etiology is unknown, although tracheobronchomegaly has been observed in patients who have Ehlers-Danlos syndrome, generalized elastolysis, marfanoid condition, or ankylosing spondylitis; as a complication of severe pulmonary fibrosis; and in many congenital syndromes involving multiple skeletal abnormalities. www.chestnet.org /education/online/pccu/vol17/lessons11_12/lesson12.php   (4251 words)

Highbeam Encyclopedia - Search Results for Kuhn, Thomas Samuel   (Site not responding. Last check: 2007-10-26) Kuhn, Thomas Samuel KUHN, THOMAS SAMUEL [Kuhn, Thomas Samuel] 1922-96, American philosopher and historian of science, b. He trained as a physicist at Harvard (Ph.D. 1949), where he taught the history of science from 1948 to 1956. Find newspaper and magazine articles plus images and maps related to "Kuhn, Thomas Samuel" at HighBeam. www.encyclopedia.com /articles/07099.html   (253 words)

Medical Dictionary: Mounier-Kuhn syndrome - WrongDiagnosis.com Mounier-Kuhn syndrome: A rare and probably congenital condition characterized by great enlargement of the lumen of the trachea and the larger bronchi. Ophanet, a consortium of European partners, currently defines a condition rare when if affects 1 person per 2,000. They list Mounier-Kuhn syndrome as a "rare disease". www.wrongdiagnosis.com /medical/mounier_kuhn_syndrome.htm   (169 words)

YoungLung.org - Providing services for teens and young adults living with chronic lung disease Another congenital cause, primary ciliary dyskinesia, occurs when the cilia of the respiratory epithelium are structurally aberrant and move abnormally. Kartagener's syndrome is a form of primary ciliary dyskinesia defined by the triad of situs inversus, sinusitis, and bronchiectasis. Humoral immunodeficiency is associated with bronchiectasis through recurrent infections of the lungs and sinuses. www.younglung.org /support/admin_diseaseview.asp?key=4   (1590 words)

Autoimmune   (Site not responding. Last check: 2007-10-26) In Loffler's syndrome patients develop transient pulmonary consolidations associated with peripheral eosinophilia and present with wheezing or a history of atopia. Goodpasteur's syndrome results from the presence of an IgG anti-glomerular/ alveolar basement membrane antibodies (detected by radioimmunoassay in over 90% of cases). Caplan's syndrome: Caplan's syndrome is characterized by rheumatoid arthritis with pulmonary rheumatic nodules in coal workers. www.indyrad.iupui.edu /public/lectures/HTML/CHEST-RM/Auto.htm   (5750 words)

Breathing Disorders I have put this on a page by itself so anybody that is not interested would not have to be bored by reading it. Most cases are sporadic and affect males Patients usually present as young adults with complaints of recurrent infections and chronic cough. Examples include the Williams-Campbell syndrome, in which there is an absence of annular bronchial cartilage, and the Mounier-Kuhn syndrome (congenital tracheobronchomegaly), in which there is a connective tissue disorder www.angelfire.com /ga/rogerspot/breathing.html   (625 words)

AHIMA - American Health Information Management Association Evans' syndrome involves a hemolytic anemia along with thrombocytopenia, related to an autoimmune process affecting both the red cells and platelets. Under the proposal, Wiskott-Aldrich syndrome would continue to be classified to code 279.12. Erythromelalgia is a rare syndrome of paroxysmal vasodilation with burning pain, increased skin temperature, and redness of the feet, and less often, the hands. www.ahima.org /dc/federal/icd9_cm_summary_april04.asp   (7006 words)

Tracheobronchial stenosis in Keutel syndrome -- Meier et al. 17 (3): 566 -- European Respiratory Journal Keutel syndrome is a rare disorder and meanwhile 17 patients Keutel syndrome is an autosomal recessive disorder and Munroe Fryns JP, van Fleteren A, Mattelaer P, van den Berghe H. Calcification of cartilages, brachytelephalangy and peripheral pulmonary stenosis: confirmation of the Keutel syndrome. erj.ersjournals.com /cgi/content/full/17/3/566   (1277 words)

ACR Learning File Web Case LA103: Annuloaortic ectasia secondary to Marfan syndrome with minimal aortic regurgitation. Case EE100: Diffuse pulmonary hemorrhage secondary to antiglomerular basement membrane disease (Goodpasture syndrome). Case JJ100: Acute chest syndrome; sickle cell anemia. www.learningfile.com /learning_file/toc.php?section=ch   (1685 words)

Chronic pulmonary suppuration -- 77 (906): 274 -- Postgraduate Medical Journal The syndrome is rare and often begins in childhood, the Mounier Kuhn syndrome: report of two cases and a review of literature. Katz I, LeVine M, Herman P. Tracheobronchomegaly (the Mounier Kuhn syndrome). pmj.bmjjournals.com /cgi/content/full/77/906/274g   (555 words)

Dorlands Medical Dictionary The prototype for mucopolysaccharidosis is Hurler's syndrome (q.v.). I (MPS I) originally, Hurler's syndrome; it now encompasses any of the forms characterized by deficiency of V former name for Scheie's syndrome, now classified as m. www.mercksource.com /pp/us/cns/cns_hl_dorlands.jspzQzpgzEzzSzppdocszSzuszSzcommonzSzdorlandszSzdorlandzSzdmd_m_21zPzhtm   (3776 words)

Diverticulosis at The Medical Dictionary Tears in the colon leading to bleeding or perforations may occur, intestinal obstruction may occur (constipation or diarrhea does not rule this possibility out), peritonitis, abscess formation, retroperitoneal fibrosis, sepsis, and fistula formation. Irritable Bowel Syndrome and Diverticulosis: A Self-Help Plan $1.84 The "Irritable bowel" diet: An ADDS dietary plan for those with irritable bowel syndrome and diverticulosis (ADDS dietary plans) $6.35 the-medical-dictionary.com /diverticulosis.htm   (790 words)

Imaging of the pulmonary manifestations of systemic disease -- Rockall et al. 77 (912): 621 -- Postgraduate Medical ... This autoimmune syndrome is characterised by lymphocytic infiltration of the lacrimal and salivary glands. The syndrome may be primary or secondary, being associated with Goodpasture's syndrome originally referred to diffuse alveolar haemorrhage occurring with rapidly progressive glomerulonephritis. pmj.bmjjournals.com /cgi/content/full/77/912/621   (5731 words)

Homo sapiens diseases - Respiratory apparatus Arnold's nerve reflex cough syndrome / ear cough : a reflex cough due to irritation of the area supplied by Arnold's nerve (the auricular branch of the vagus nerve); this area is the posterior and inferior portion of the external auditory canal and the posterior half of the tympanic membrane. Leredde's syndrome : severe dyspnea on exertion, combined with advanced emphysema and recurrent attacks of acute febrile bronchitis; seen in children with congenital syphilis (Treponema pallidum subsp. Citelli's syndrome : mental dullness, loss of power of concentration, and drowsiness or insomnia, seen in persons with adenoids or sinus infection. focosi.immunesig.org /pathohomotissuerespiratory.html   (7950 words)

ICD-9-CM Disease Index: M Marie-Bamberger disease or syndrome (hypertrophic) (pulmonary) (secondary) 731.2 Mikulicz's disease or syndrome (dryness of mouth, absent or decreased lacrimation) 527.1 Milkman (-Looser) disease or syndrome (osteomalacia with pseudofractures) 268.2 www.dmi.columbia.edu /hripcsak/icd9/2indexm.html   (818 words)

Navigating the Thoracic Inlet -- Chiles et al. 19 (5): 1161 -- RadioGraphics   (Site not responding. Last check: 2007-10-26) Thoracic outlet syndrome refers to symptoms of compression of   Retropharyngeal space abscess in a 42-year-old man with Down syndrome, sore throat, and dyspnea. Axial contrast-enhanced CT scan shows a large fluid collection in the retropharyngeal space (A) with peripheral enhancement and an air-fluid level. intl-radiographics.rsnajnls.org /cgi/content/full/19/5/1161   (4923 words)

Tracheobronchomegaly--the Mounier-Kuhn syndrome: report of two cases and review of the literature -- Van Schoor et al. ... Tracheobronchomegaly--the Mounier-Kuhn syndrome: report of two cases and review of the literature -- Van Schoor et al. Tracheobronchomegaly--the Mounier-Kuhn syndrome: report of two cases and review of the literature Pulmonary transplantation in Mounier-Kuhn syndrome: A case report erj.ersjournals.com /cgi/content/abstract/4/10/1303   (203 words)

AR Online » CT & CTA » Chest » Right paratracheal air cyst/tracheal diverticulum Histologically, they are lined by respiratory epithelium; however, no mucous glands, smooth muscle, or cartilage are found in the wall. Mounier-Kuhn syndrome is a rare disorder characterized by multiple tracheal diverticula with associated marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent lower respiratory infections. The diagnosis of tracheal diverticula is relatively straightforward and can be made radiographically. www.appliedradiology.com /case/case.asp?Id=410&IssueID=114&CatID=43&SubCatID=102&ThreadID=&Quiz=   (1408 words)

Tracheobronchomegaly (Mounier-Kuhn's syndrome) - MayoClinic.com Mayo Clinic pulmonologist Edward Rosenow, M.D., and colleagues answer select questions from readers. Mounier-Kuhn's syndrome is a rare lung disorder characterized by marked widening (dilation) of the trachea and sometimes the larger bronchial tubes. Doctors may also refer to this disorder as tracheobronchomegaly. www.mayoclinic.com /health/lung-disease/AN00906   (233 words)

meJane Legal Transcriptionist Manual - Medical Glossary   (Site not responding. Last check: 2007-10-26) Pott's fracture - Fracture of the lower part of the fibula with injury to lower tibial articulation Radial tunnel syndrome - Of or pertaining to the area near the radius (wrist). Syndrome - A set of symptoms that characterize a disorder or disease. www.netrover.com /~bouletj/glossaries/medical.html   (938 words)

A 60-Year-Old Man With Recurrent Pneumonias -- Schwarz 119 (5): 1590 -- Chest Answer: B. The underlying pathologic finding is poorly formed or absent bronchial cartilage. syndrome, another cause of bronchiectasis and progressive obstructive The Mounier-Kuhn syndrome is found in patients with Ehlers-Danlos syndrome, www.chestjournal.org /cgi/content/full/119/5/1590   (462 words)

BRONCHIECTASIE   (Site not responding. Last check: 2007-10-26) -antitrypsin (AAT) deficiency, inflammatory bowel disease, and Young’s syndrome. Williams-Campbell syndrome, Mounier-Kuhn syndrome, pulmonary sequestration, pulmonary artery aneurysm, yellow nail syndrome For most patients, symptoms of bronchiectasis develop in childhood. www.chirurgiatoracica.org /bronchiectasie1.htm   (1478 words)

Mammography and Other Problems In a letter to the American Journal of Roentgenology ("National Conference on Breast Cancer: Adequacy of Mammography Training," 133, No. 1 [July 1979]: 161) Dr. Marc J. Homer of the New England Medical Center Hospital stated: "Not too long ago I prepared for my oral boards in radiology. Though subjects as esoteric as congenital hypophosphatemia and the Mounier-Kuhn syndrome were covered. Though last year I saw more breast cancers on my viewbox than all the colon, stomach, and kidney cancers combined, I never had to interpret a single mammogram as a resident. implants.clic.net /tony/Corner/E/0228.html   (1236 words)

Lung Diseases (Print Version) Goodpasture's Syndrome (National Institute of Diabetes and Digestive and Kidney Diseases) - http://kidney.niddk.nih.gov/kudiseases/pubs/goodpasture/ Loeffler's Syndrome (Pulmonary Eosinophilia) (Mayo Foundation for Medical Education and Research) - http://www.mayoclinic.com/health/pulmonary-eosinophilia/AN00844 Tracheobronchomegaly (Mounier-Kuhn's Syndrome) (Mayo Foundation for Medical Education and Research) - http://www.mayoclinic.com/health/lung-disease/AN00906 www.nlm.nih.gov /medlineplus/print/lungdiseases.html   (906 words)

Respiratory Diseases Respiratory Diseases Health Topics - MedicineOnline.com - Medical Information Loeffler's Syndrome (Pulmonary Eosinophilia) (Mayo Foundation for Medical Education and Research) Tracheobronchomegaly (Mounier-Kuhn's Syndrome) (Mayo Foundation for Medical Education and Research) Respiratory Distress Syndrome of the Newborn (American Lung Association) www.medicineonline.com /healthtopics/topics/Lung_Diseases/Respiratory_Diseases   (610 words)

An Investigation into Causative Factors in Patients with Bronchiectasis -- PASTEUR et al. 162 (4): 1277 -- American ... Five patients (3%) were shown to have Young's syndrome (15) This syndrome has been linked to mercury poisoning Kuhn syndrome) (17), a congenital deficiency of cartilage. ajrccm.atsjournals.org /cgi/content/full/162/4/1277   (5326 words)

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